Interstitial lung disease
Etiology
Drug-related
- Amiodarone
 - Antibacterials (nitrofurantoin, sulfonamides)
 - Antineoplastics (bleomycin, cyclophosphamide, methotrexate, nitrosoureas)
 - Antirheumatics (gold salts, penicillamine)
 - Phenytoin
 
- Inorganic dust (asbestos, silica, hard metals, beryllium)
 - Organic dust or hypersensitivity pneumonitis (thermophilic actinomycetes, avian antigens, Aspergillus spp.)
 - Gases, fumes, vapors (chlorine, isocyanates, paraquat, sulfur dioxide)
 - Ionizing radiation
 - Talc (injection drug users)
 
- Disseminated fungus (coccidioidomycosis, blastomycosis, histoplasmosis)
 - Disseminated mycobacteria
 - Pneumocystis jiroveci pneumonia
 - Viruses
 
- Idiopathic fibrosing interstitial pneumonia [idiopathic pulmonary fibrosis (IPF)]: 
- Acute interstitial pneumonia (AIP)
 
- Desquamative interstitial pneumonia (DIP)
 
- Nonspecific interstitial pneumonitis (NSIP)
 
- Usual interstitial pneumonia (UIP)
 
- Respiratory bronchiolitis-associated interstitial lung disease (RB-ILD)
 
 - Bronchiolitis obliterans-organizing pneumonia (BOOP)
 
- Acute respiratory distress syndrome (ARDS)
 - Amyloidosis
 - Ankylosing spondylitis
 - Autoimmune disease: dermatomyositis, polymyositis, rheumatoid arthritis, systemic sclerosis (scleroderma), systemic lupus erythematosus
 - Chronic eosinophilic pneumonia
 - Goodpasture's syndrome
 - Idiopathic pulmonary hemosiderosis
 - Inflammatory bowel disease
 - Eosinophilic granuloma (Langerhans cell histiocytosis, histiocytosis X)
 - Lymphangitic carcinomatosis
 - Lymphangioleiomyomatosis (LAM)
 - Pulmonary edema
 - Pulmonary venous hypertension
 - Sarcoidosis
 - Wegener's granulomatosis
 
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Last updated: December 1, 2014
Citation
Zeiger, Roni F.. "Interstitial Lung Disease." Diagnosaurus, 4th ed., McGraw-Hill Education, 2014. Emergency Central, emergency.unboundmedicine.com/emergency/view/Diagnosaurus/114753/0/Interstitial_lung_disease. 
Zeiger RFR. Interstitial lung disease. Diagnosaurus. McGraw-Hill Education; 2014. https://emergency.unboundmedicine.com/emergency/view/Diagnosaurus/114753/0/Interstitial_lung_disease. Accessed November 3, 2025.
Zeiger, R. F. (2014). Interstitial lung disease. In Diagnosaurus (4th ed.). McGraw-Hill Education. https://emergency.unboundmedicine.com/emergency/view/Diagnosaurus/114753/0/Interstitial_lung_disease
Zeiger RFR. Interstitial Lung Disease [Internet]. In: Diagnosaurus. McGraw-Hill Education; 2014. [cited 2025 November 03]. Available from: https://emergency.unboundmedicine.com/emergency/view/Diagnosaurus/114753/0/Interstitial_lung_disease.
* Article titles in AMA citation format should be in sentence-case
TY  -  ELEC
T1  -  Interstitial lung disease
ID  -  114753
A1  -  Zeiger,Roni F,
Y1  -  2014/12/01/
BT  -  Diagnosaurus
UR  -  https://emergency.unboundmedicine.com/emergency/view/Diagnosaurus/114753/0/Interstitial_lung_disease
PB  -  McGraw-Hill Education
ET  -  4
DB  -  Emergency Central
DP  -  Unbound Medicine
ER  -  

Diagnosaurus

